医学
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10 篇有效样本 · 按发表日期由新到旧排列
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Lung mucus burden and treatment response assessed by MRI in the post-modulator era
作者Alexander M Matheson; Evan Prather; Matthew M Willmering; Jaime Mata; Giles Santyr; Felix A Ratjen; Elizabeth L Kramer; Zackary I Cleveland; Jason C Woods
作者单位Center for Pulmonary Imaging Research, Cincinnati Children's Hospital, Cincinnati, OH, United States; Pulmonary Medicine, Cincinnati Children's Hospital, Cincinnati, OH, United States; Department of Pediatrics, The University of Cincinnati, Cincinnati, OH, United States; College of Medicine, The University of Cincinnati, Cincinnati, OH, United States; University of Virginia, Virginia, VA, United States; Department of Radiology, The Hospital for Sick Children, Toronto, ON, Canada; Translational Medicine Program, The Hospital for Sick Children, Toronto, ON, Canada
Expiratory lung MRI: a simple, sensitive method to quantify and visualise regional gas trapping in cystic fibrosis
作者Amy V Simmons; Laurie J Smith; Zoe Somerville; Hannah Faulke; William Clark; David Hughes; Ina Aldag; Noreen West; Alberto M Biancardi; Jim M Wild; Neil J Stewart
作者单位POLARIS, Division of Clinical Medicine, Faculty of Health, The University of Sheffield, United Kingdom; INSIGNEO Institute for in silico Medicine, The University of Sheffield, Sheffield, United Kingdom; Sheffield Children’s Hospital NHS Foundation Trust, Sheffield, United Kingdom
International Delphi consensus recommendations for the follow-up of children born to people with CF and exposed to CFTR modulators in utero or through breastfeeding; endorsed by the European Cystic Fibrosis Society
作者Idan Bokobza; Traci M. Kazmerski; Louise Thomson; Rebecca V. Scott; Amy Downes; Claire L. Hogg; Siân Bentley; Elaine Bowman; Lynn Sinitsky; Olivia Beaumont; Ladina Weitnauer; Quitterie Reynaud; Philippe Reix; Imogen Felton; Jane C. Davies
作者单位Imperial College London, Imperial Biomedical Research Centre, National Heart & Lung Institute, London, United Kingdom; Royal Brompton & Harefield Hospitals, part of Guys and St Thomas' Hospital NHS Foundation Trust, Department of Paediatric Respiratory Medicine, London, United Kingdom; University of Pittsburgh School of Medicine, Department of Pediatrics, Pittsburgh, United States; Royal Hospital for Children Glasgow, Department of Paediatric Respiratory Medicine, Glasgow, United Kingdom; Chelsea & Westminster Hospital, Department of Diabetes & Endocrinology, London, United Kingdom; Royal Brompton & Harefield Hospitals, part of Guys and St Thomas' Hospital NHS Foundation Trust, Adult Cystic Fibrosis Centre, London, United Kingdom; Imperial College London, Department of Metabolism, Digestion and Reproduction, London, United Kingdom; Royal Brompton & Harefield Hospitals, part of Guys and St Thomas' Hospital NHS Foundation Trust, Pharmacy Department, London, United Kingdom; West Hertfordshire Teaching Hospitals NHS Trust, Watford, United Kingdom; King's College Hospital, London, United Kingdom; Centre Hospitalier Universitaire Vaudois, Adult CF centre, Lausanne, Switzerland; Hospices Civils de Lyon – Hôpital Lyon Sud, Adult Cystic Fibrosis Center, Internal Medicine and Vascular Pathology Department, Lyon, France; University Claude Bernard Lyon 1, Research on Healthcare Performance (RESHAPE), INSERM U1290, Lyon, France; Hospices civils de Lyon - Hôpital Femme Mère Enfant, Centre de ressources et de compétences pour la mucoviscidose, Lyon, France
Dupilumab in the treatment of severe chronic rhinosinusitis with nasal polyps (CRSwNP) in cystic fibrosis patients
作者Attilio Di Girolamo; Mattia Cristallo; Michelina Francesca Daddato; Federico Spataro; Giuseppina Leonetti; Pamela Vitullo; Eustachio Nettis
作者单位Department of Precision and Regenerative Medicine and Ionian Area, Regional Reference Center for Allergic and Immunological Diseases, Bari, Italy; Department of Precision and Regenerative Medicine and Ionian Area - DiMePRe-J, Post Graduate School of Allergy and Clinical Immunology, Guido Baccelli Unit of Internal Medicine, University of Bari Aldo Moro, 70124 Bari, Italy; Department of Precision and Regenerative Medicine and Ionian Area - DiMePRe-J, Section of Pharmacology, University of Bari Aldo Moro, 70124 Bari, Italy; Pediatric Cystic Fibrosis Centre, Azienda Universitaria Ospedaliera Consorziale Policlinico, Bari, Italy; Cystic Fibrosis Support Center, Ospedale G. Tatarella di Cerignola, Cerignola, Italy
Investigation of HE4 expression concerning epithelial-mesenchymal transition (EMT) in cystic fibrosis epithelial cells
作者Marianna Pócsi; György Jázon Balla; Ferenc Fenyvesi; Ágnes Rusznyák; Zsolt Fejes; István Balogh; Milan Macek; Margarida D. Amaral; Béla Nagy
作者单位Department of Laboratory Medicine, Faculty of Medicine, University of Debrecen, Debrecen, Hungary; Department of Molecular and Nanopharmaceutics, Faculty of Pharmacy, University of Debrecen, Debrecen, Hungary; Division of Clinical Genetics, Department of Laboratory Medicine, Faculty of Medicine, University of Debrecen, Debrecen, Hungary; Department of Biology and Medical Genetics, 2nd Faculty of Medicine and Motol University Hospital, Charles University, Prague, Czech Republic; BioISI- Biosystems & Integrative Sciences Institute, Faculty of Sciences, University of Lisboa, Lisboa, Portugal
Altered responsiveness to photic stimuli contribute to circadian disruption in cystic fibrosis
作者Danica F. Patton-Parfyonov; Eden N. Kenner; Deborah A. Corey; Thomas J. Kelley; Rebecca Darrah
作者单位Department of Genetics and Genome Sciences, School of Medicine, Case Western Reserve University, Cleveland, OH 44106
Effects of Elexacaftor/Tezacaftor/Ivacaftor on cough frequency, physical activity patterns, and sleep quality in adolescents and adults with cystic fibrosis
作者Eva Van Braeckel; Andrew T. Braun; Nicholas J. Simmonds; Peter J. Barry; Jane C. Davies; Marie E. Egan; Allen Lapey; Marcus A. Mall; Edward F. McKone; Daniel Peckham; Marijke Proesmans; Bonnie Ramsey; Saioa Vicente Santamaria; Daniel Smith; Jennifer L. Taylor-Cousar; Elizabeth Tullis; Elke De Wachter; Nick Withers; Neil Ahluwalia; Sarah Conner; Mark Jennings; Yiyue Lou; Tanya G. Weinstock; Dominic Keating
作者单位Department of Respiratory Medicine, Ghent University Hospital, Ghent, Belgium; Department of Internal Medicine and Paediatrics, Faculty of Medicine and Health Sciences, Ghent University, Ghent, Belgium; University of Wisconsin School of Medicine and Public Health, Madison, WI, USA; National Heart and Lung Institute, Imperial College London UK, Royal Brompton Hospital, part of Guy's and St Thomas' NHS Foundation Trust, London, UK; Manchester University NHS Foundation Trust, Manchester, UK; Division of Infection, Immunity and Respiratory Medicine, University of Manchester, Manchester, UK; Yale University, New Haven, CT, USA; Massachusetts General Hospital, Boston, MA, USA; Department of Pediatric Respiratory Medicine, Immunology and Critical Care Medicine, Charité - Universitätsmedizin Berlin, Berlin, Germany; German Center for Lung Research (DZL), associated partner site, Berlin, Germany; German Center for Child and Adolescent Health (DZKJ), partner site Berlin, Berlin, Germany; Cluster of Excellence ImmunoPreCept, Charité - Universitätsmedizin Berlin, Berlin, Germany; St Vincent’s University Hospital, Dublin, Ireland; St James’s University Hospital, Leeds, UK; University Hospital of Leuven, Leuven, Belgium; Seattle Children’s Hospital, Seattle, WA, USA; Hospital Ramón y Cajal, Madrid, Spain; The Prince Charles Hospital, Brisbane, Queensland, Australia; National Jewish Health, Denver, CO, USA; St Michael’s Hospital, Toronto, Ontario, Canada; Universitair Ziekenhuis Brussel, Vrije Universiteit Brussel, Brussels, Belgium; Royal Devon United Hospital NHS Foundation Trust, Exeter, UK; Vertex Pharmaceuticals Incorporated, Boston, MA, USA; Alfred Health, and Monash University, Melbourne, Victoria, Australia
Treatment with elexacaftor/tezacaftor/ivacaftor does not alter SpiroNose-derived electronic breath profiles in children with cystic fibrosis
作者Elias Seidl; Andrew Zikic; Srdjan Micic; Rianne de Vries; Julie Avolio; Alexander Moeller; Felix Ratjen; Hartmut Grasemann
作者单位Department of Respiratory Medicine, University Children's Hospital Zurich, Zurich, Switzerland; Division of Respiratory Medicine, Department of Pediatrics, The Hospital for Sick Children, Toronto, Canada; Breathomix BV, Bargelaan 200, Leiden, CW 2333, The Netherlands; Translational Medicine, Research Institute, Hospital for Sick Children, Toronto, ON M5G 1 × 8, Canada and University of Toronto, Toronto, Canada
Apical hyperosmotic challenge upregulates aquaporin-3 in human airway epithelia
作者Alexander Sauter; Oliver H Wittekindt; Lara Gutjahr; Ronja Rössel; Manfred Frick; Sebastian FN Bode; Hanna Schmidt
作者单位Institute of General Physiology, Ulm University; Albert-Einstein-Allee 11 89075, Ulm, Germany; Department of Pediatrics and Adolescent Medicine, Ulm University Medical Center; Eythstraße 24 89075, Ulm, Germany
Microbiological outcomes associated with Burkholderia species in people with cystic fibrosis receiving CFTR modulator therapy
作者Timothy Riddles; Daniel Smith; David W Reid; Daniel Henderson; Arianne J Blanco; Vanessa Moore; Michelle Wood; Ieuan E S Evans
作者单位Adult Cystic Fibrosis Centre, The Prince Charles Hospital, Brisbane, QLD, Australia; Faculty of Medicine, University of Queensland, QLD, Brisbane, Australia; Lung Inflammation & Infection, QIMR Berghofer Medical Research Institute, Brisbane, QLD, Australia; Department of Microbiology, Royal Brisbane Women’s Hospital, Brisbane, QLD, Australia
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